Description
This panel contains genes associated with hyperparathyroidism 
(and includes some cancer predisposition disorders). 

It includes genes from the Genomics England PanelApp 'familial hyperparathyroidism or hypocalciuric hypercalcaemia' panel V3.6.

5 reviewers

  • Alison Yeung (Victorian Clinical Genetics Services)

  • Ain Roesley (Victorian Clinical Genetics Services)

  • Chirag Patel (Genetic Health Queensland)

  • Bryony Thompson (Royal Melbourne Hospital)

  • Zornitza Stark (Victorian Clinical Genetics Services)

6 Entities

6 reviewed, 6 green

List Entity Reviews Mode of inheritance Details
6 Entitiess
Green Green List (high evidence)
CASR
1 review
1 green
BOTH monoallelic and biallelic, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Genomics England PanelApp
Phenotypes
  • Neonatal severe primary hyperparathyroidism, MONDO:0009397
Tags
Green Green List (high evidence)
CDC73
1 review
1 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
Phenotypes
  • Hyperparathyroidism-jaw tumour syndrome, MIM# 145001
  • Hyperparathyroidism, familial primary, MIM# 145000
Tags
Green Green List (high evidence)
CDKN1B
1 review
1 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
Phenotypes
  • Multiple endocrine neoplasia type 4, MEN4, OMIM #610755
Tags
Green Green List (high evidence)
GCM2
1 review
1 green
MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Sources
  • Expert Review Green
  • Literature
Phenotypes
  • Hyperparathyroidism 4, OMIM #617343
Tags
Green Green List (high evidence)
MEN1
2 reviews
2 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert list
  • Expert Review Green
Phenotypes
  • Multiple endocrine neoplasia 1 MIM#131100
Tags
Green Green List (high evidence)
RET
2 reviews
2 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert list
  • Expert Review
  • Expert Review Green
Phenotypes
  • Multiple endocrine neoplasia IIA, MIM# 171400
  • Multiple endocrine neoplasia IIB, MIM# 162300
Tags

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