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Hereditary Spastic Paraplegia v2.7 AARS2 Bryony Thompson Marked gene: AARS2 as ready
Hereditary Spastic Paraplegia v2.7 AARS2 Bryony Thompson Gene: aars2 has been classified as Green List (High Evidence).
Hereditary Spastic Paraplegia v2.7 AARS2 Bryony Thompson Classified gene: AARS2 as Green List (high evidence)
Hereditary Spastic Paraplegia v2.7 AARS2 Bryony Thompson Gene: aars2 has been classified as Green List (High Evidence).
Hereditary Spastic Paraplegia v2.6 AARS2 Bryony Thompson gene: AARS2 was added
gene: AARS2 was added to Hereditary Spastic Paraplegia. Sources: Literature
Mode of inheritance for gene: AARS2 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: AARS2 were set to 35084689; 34285876; 31388113; 30272204; 28322004; 27749956
Phenotypes for gene: AARS2 were set to Mitochondrial disease, MONDO:0044970; hereditary diffuse leukoencephalopathy with axonal spheroids and pigmented glia, MONDO:0009096; ovarioleukodystrophy, MONDO:0020506
Review for gene: AARS2 was set to GREEN
Added comment: Adult-onset hereditary diffuse leukoencephalopathy with axonal spheroids and pigmented glia (ALSP), an autosomal recessive loss‑of‑function AARS2 disease, can present with spastic paraparesis, cognitive decline and characteristic MRI changes.
Sources: Literature