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Ataxia v2.20 ACOX1 Sangavi Sivagnanasundram Classified gene: ACOX1 as Amber List (moderate evidence)
Ataxia v2.20 ACOX1 Sangavi Sivagnanasundram Gene: acox1 has been classified as Amber List (Moderate Evidence).
Ataxia v2.19 ACOX1 Sangavi Sivagnanasundram gene: ACOX1 was added
gene: ACOX1 was added to Ataxia. Sources: Literature
Mode of inheritance for gene: ACOX1 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: ACOX1 were set to 38923841; 37846133
Phenotypes for gene: ACOX1 were set to Mitchell syndrome, MONDO:0030073
Review for gene: ACOX1 was set to AMBER
Added comment: Three unrelated individuals presenting with Mitchell syndrome, characterised by progressive gait ataxia, sensorineural hearing loss, visual impairment, ichthyosis and polyneuropathy.
They all carry the same heterozygous missense variant c.710A>G, p.Asn237Ser, which is absent in gnomAD v4.1.
Sources: Literature