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Arthrogryposis v0.640 ATN1 Zornitza Stark Marked gene: ATN1 as ready
Arthrogryposis v0.640 ATN1 Zornitza Stark Gene: atn1 has been classified as Green List (High Evidence).
Arthrogryposis v0.640 ATN1 Zornitza Stark Classified gene: ATN1 as Green List (high evidence)
Arthrogryposis v0.640 ATN1 Zornitza Stark Gene: atn1 has been classified as Green List (High Evidence).
Arthrogryposis v0.639 ATN1 Zornitza Stark gene: ATN1 was added
gene: ATN1 was added to Arthrogryposis. Sources: Literature
Mode of inheritance for gene: ATN1 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: ATN1 were set to 34212383
Phenotypes for gene: ATN1 were set to Congenital hypotonia, epilepsy, developmental delay, and digital anomalies, MIM# 618494
Review for gene: ATN1 was set to GREEN
Added comment: Nine individuals reported with de novo missense or in-frame deletions/duplications within the "HX motif" of exon 7 of ATN1 and presenting with 'congenital hypotonia, epilepsy, developmental delay, and digital anomalies (CHEDDA)' syndrome, distinct from dentatorubral-pallidoluysian atrophy (DRPLA) secondary to expansion variants in exon 5 of ATN1.

Arthrogryposis is a feature.
Sources: Literature