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Skeletal dysplasia v0.444 DDX58 Zornitza Stark Marked gene: DDX58 as ready
Skeletal dysplasia v0.444 DDX58 Zornitza Stark Gene: ddx58 has been classified as Green List (High Evidence).
Skeletal dysplasia v0.444 DDX58 Zornitza Stark changed review comment from: Comment when marking as ready: New HGNC approved name is RIGI.; to: New HGNC approved name is RIGI.

Syndrome with significant skeletal involvement.
Skeletal dysplasia v0.444 Zornitza Stark Copied gene DDX58 from panel Mendeliome
Skeletal dysplasia v0.444 DDX58 Zornitza Stark gene: DDX58 was added
gene: DDX58 was added to Skeletal dysplasia. Sources: Expert Review Green,Victorian Clinical Genetics Services
new gene name tags were added to gene: DDX58.
Mode of inheritance for gene: DDX58 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: DDX58 were set to 25620203; 30574673; 33495304
Phenotypes for gene: DDX58 were set to Singleton-Merten syndrome 2, MIM# 616298
Mode of pathogenicity for gene: DDX58 was set to Loss-of-function variants (as defined in pop up message) DO NOT cause this phenotype - please provide details in the comments