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Hereditary Neuropathy v2.19 ERCC4 Zornitza Stark Marked gene: ERCC4 as ready
Hereditary Neuropathy v2.19 ERCC4 Zornitza Stark Gene: ercc4 has been classified as Green List (High Evidence).
Hereditary Neuropathy v2.19 ERCC4 Zornitza Stark Classified gene: ERCC4 as Green List (high evidence)
Hereditary Neuropathy v2.19 ERCC4 Zornitza Stark Gene: ercc4 has been classified as Green List (High Evidence).
Hereditary Neuropathy v2.2 ERCC4 Sangavi Sivagnanasundram gene: ERCC4 was added
gene: ERCC4 was added to Hereditary Neuropathy. Sources: Literature
Mode of inheritance for gene: ERCC4 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: ERCC4 were set to 38040034; 35699229
Phenotypes for gene: ERCC4 were set to ERCC4-related neuropathy MONDO:0100545
Review for gene: ERCC4 was set to GREEN
Added comment: PMID 35699229 reports 8 individuals with a complex neurological disorder (progressive cerebellar syndrome, ataxia, dementia, chorea, spasticity) and biallelic variants in ERCC4.
7 of the reported affected individuals presented with peripheral neuropathy.
Sources: Literature