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Mendeliome v1.3754 ESRRG Zornitza Stark Marked gene: ESRRG as ready
Mendeliome v1.3754 ESRRG Zornitza Stark Gene: esrrg has been classified as Green List (High Evidence).
Mendeliome v1.3754 ESRRG Zornitza Stark Classified gene: ESRRG as Green List (high evidence)
Mendeliome v1.3754 ESRRG Zornitza Stark Gene: esrrg has been classified as Green List (High Evidence).
Mendeliome v1.3753 ESRRG Zornitza Stark gene: ESRRG was added
gene: ESRRG was added to Mendeliome. Sources: Literature
Mode of inheritance for gene: ESRRG was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: ESRRG were set to 41265451
Phenotypes for gene: ESRRG were set to Movement disorder, MONDO:0005395, ESRRG-related
Review for gene: ESRRG was set to GREEN
Added comment: Eight individuals from seven unrelated families reported with heterozygous, mostly de novo variants in ESRRG: c.410G>A (p.Gly137Glu), c.446A>G (p.Lys149Arg), c.539G>A (p.Cys180Tyr), c.550C>T (p.Arg184Cys), c.1346T>G (p.Leu449Arg), and c.1352dup (p.Leu451Phefs∗38). All individuals had motor developmental delay, muscular hypotonia, and eye movement disorders, as well as congenital ataxia or gait imbalance. Other symptoms included joint hyperflexibility, dysarthria, myopia, and growth delay. Supportive functional data.
Sources: Literature