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Cardiomyopathy_Paediatric v1.10 FXN_FRDA_GAA Zornitza Stark Marked STR: FXN_FRDA_GAA as ready
Cardiomyopathy_Paediatric v1.10 FXN_FRDA_GAA Zornitza Stark Str: fxn_frda_gaa has been classified as Green List (High Evidence).
Cardiomyopathy_Paediatric v1.10 Zornitza Stark Copied STR FXN_FRDA_GAA from panel Mendeliome
Cardiomyopathy_Paediatric v1.10 FXN_FRDA_GAA Zornitza Stark STR: FXN_FRDA_GAA was added
STR: FXN_FRDA_GAA was added to Cardiomyopathy_Paediatric. Sources: Expert list,Expert Review Green,Expert Review Green,Expert list
paediatric-onset tags were added to STR: FXN_FRDA_GAA.
Mode of inheritance for STR: FXN_FRDA_GAA was set to BIALLELIC, autosomal or pseudoautosomal
Publications for STR: FXN_FRDA_GAA were set to 20301458; 8596916
Phenotypes for STR: FXN_FRDA_GAA were set to Friedreich ataxia MIM#229300
Cardiomyopathy_Paediatric v1.9 FXN Zornitza Stark Marked gene: FXN as ready
Cardiomyopathy_Paediatric v1.9 FXN Zornitza Stark Gene: fxn has been classified as Green List (High Evidence).
Cardiomyopathy_Paediatric v1.9 FXN Zornitza Stark Classified gene: FXN as Green List (high evidence)
Cardiomyopathy_Paediatric v1.9 FXN Zornitza Stark Gene: fxn has been classified as Green List (High Evidence).
Cardiomyopathy_Paediatric v1.8 FXN Zornitza Stark Tag STR tag was added to gene: FXN.
Cardiomyopathy_Paediatric v1.8 FXN Zornitza Stark gene: FXN was added
gene: FXN was added to Cardiomyopathy_Paediatric. Sources: Expert Review
Mode of inheritance for gene: FXN was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: FXN were set to 41432640; 40880907; 38396238; 34610949; 32999401
Phenotypes for gene: FXN were set to Friedreich ataxia, MIM# 229300
Review for gene: FXN was set to GREEN
Added comment: Well established gene-disease association.

Hypertrophic cardiomyopathy is a feature. Onset in adolescence/childhood.
Sources: Expert Review