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Skeletal dysplasia v1.0 GHRHR Gene migrated from ENSG00000106128 to ENSG00000106128 (gene set migration)
Skeletal dysplasia v0.454 GHRHR Zornitza Stark reviewed gene: GHRHR: Rating: GREEN; Mode of pathogenicity: None; Publications: ; Phenotypes: ; Mode of inheritance: None
Skeletal dysplasia v0.454 GHRHR Sangavi Sivagnanasundram Classified gene: GHRHR as Green List (high evidence)
Skeletal dysplasia v0.454 GHRHR Sangavi Sivagnanasundram Gene: ghrhr has been classified as Green List (High Evidence).
Skeletal dysplasia v0.453 GHRHR Sangavi Sivagnanasundram Classified gene: GHRHR as Red List (low evidence)
Skeletal dysplasia v0.453 GHRHR Sangavi Sivagnanasundram Gene: ghrhr has been classified as Red List (Low Evidence).
Skeletal dysplasia v0.452 GHRHR Sangavi Sivagnanasundram gene: GHRHR was added
gene: GHRHR was added to Skeletal dysplasia. Sources: Other
Mode of inheritance for gene: GHRHR was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: GHRHR were set to PMID: 10084571, 8391647, 24450934
Phenotypes for gene: GHRHR were set to isolated growth hormone deficiency type IB MONDO:0013006
Review for gene: GHRHR was set to GREEN
Added comment: Isolated growth hormone deficiency type IV (IGHD4) is characterised by early and severe growth failure (height SDS up to -7.4), a blunted growth hormone (GH) response to different provocation tests and low insulin-like growth factor-I and IGF-binding protein-3 concentrations, and a good response to growth hormone treatment.

Skeletal dysplasia/ delayed bone age is a feature of this condition.
Sources: Other