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Hereditary Neuropathy v2.63 GLDN Zornitza Stark Marked gene: GLDN as ready
Hereditary Neuropathy v2.63 GLDN Zornitza Stark Gene: gldn has been classified as Green List (High Evidence).
Hereditary Neuropathy v2.53 GLDN Sangavi Sivagnanasundram Classified gene: GLDN as Green List (high evidence)
Hereditary Neuropathy v2.53 GLDN Sangavi Sivagnanasundram Gene: gldn has been classified as Green List (High Evidence).
Hereditary Neuropathy v2.52 GLDN Sangavi Sivagnanasundram gene: GLDN was added
gene: GLDN was added to Hereditary Neuropathy. Sources: Literature
Mode of inheritance for gene: GLDN was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: GLDN were set to 35740734; 28726266; 27616481
Phenotypes for gene: GLDN were set to lethal congenital contracture syndrome 11, MONDO:0014965
Review for gene: GLDN was set to GREEN
Added comment: Biallelic GLDN variants are associated with lethal congenital contracture syndrome 11 (LCCS11) – a severe arthrogryposis multiplex congenita with peripheral neuropathy, respiratory insufficiency and polyhydramnios.

Neuropathy is a presenting feature of this condition. >4 unrelated families presented with neuropathy/ abnormal transmission electron microscopy findings
Sources: Literature