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Cardiomyopathy_Paediatric v1.143 HADHA Zornitza Stark Marked gene: HADHA as ready
Cardiomyopathy_Paediatric v1.143 HADHA Zornitza Stark Gene: hadha has been classified as Green List (High Evidence).
Cardiomyopathy_Paediatric v1.143 HADHA Zornitza Stark Phenotypes for gene: HADHA were changed from Trifunctional protein deficiency 609015; Mitochondrial trifunctional protein deficiency (Disorders of mitochondrial fatty acid oxidation); Mitochondrial Trifunctional Protein deficiency; Liver disease, hypotonia, hypoketotic hypoglycaemia, neuropathy, lactic acidosis, retinopathy, hypoparathyroidism; HCM; Long chain 3-hydroxyacyl-CoA dehydrogenase deficiency (LCHADD) to mitochondrial trifunctional protein deficiency, MONDO:0012172
Cardiomyopathy_Paediatric v1.142 HADHA Zornitza Stark Publications for gene: HADHA were set to 27604308
Cardiomyopathy_Paediatric v1.141 HADHA Zornitza Stark reviewed gene: HADHA: Rating: GREEN; Mode of pathogenicity: None; Publications: 39088276, 37754774, 35677112, 32999401, 28515471; Phenotypes: mitochondrial trifunctional protein deficiency, MONDO:0012172; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Cardiomyopathy_Paediatric v1.0 HADHA Gene migrated from ENSG00000084754 to ENSG00000084754 (gene set migration)
Cardiomyopathy_Paediatric v0.134 HADHA Zornitza Stark Tag treatable tag was added to gene: HADHA.
Cardiomyopathy_Paediatric v0.0 HADHA Zornitza Stark gene: HADHA was added
gene: HADHA was added to Cardiomyopathy_Paediatric. Sources: NHS GMS,MetBioNet,Expert Review Green
Mode of inheritance for gene: HADHA was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: HADHA were set to 27604308
Phenotypes for gene: HADHA were set to Trifunctional protein deficiency 609015; Mitochondrial trifunctional protein deficiency (Disorders of mitochondrial fatty acid oxidation); Mitochondrial Trifunctional Protein deficiency; Liver disease, hypotonia, hypoketotic hypoglycaemia, neuropathy, lactic acidosis, retinopathy, hypoparathyroidism; HCM; Long chain 3-hydroxyacyl-CoA dehydrogenase deficiency (LCHADD)