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Pulmonary Fibrosis_Interstitial Lung Disease v0.186 IARS Zornitza Stark Marked gene: IARS as ready
Pulmonary Fibrosis_Interstitial Lung Disease v0.186 IARS Zornitza Stark Gene: iars has been classified as Green List (High Evidence).
Pulmonary Fibrosis_Interstitial Lung Disease v0.186 IARS Zornitza Stark Classified gene: IARS as Green List (high evidence)
Pulmonary Fibrosis_Interstitial Lung Disease v0.186 IARS Zornitza Stark Gene: iars has been classified as Green List (High Evidence).
Pulmonary Fibrosis_Interstitial Lung Disease v0.185 IARS Zornitza Stark gene: IARS was added
gene: IARS was added to Pulmonary Fibrosis_Interstitial Lung Disease. Sources: Literature
Mode of inheritance for gene: IARS was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: IARS were set to 40635052; 39950113
Phenotypes for gene: IARS were set to Growth retardation, impaired intellectual development, hypotonia, and hepatopathy, MIM#617093
Review for gene: IARS was set to GREEN
Added comment: PMID 39950113 reports an infant with biallelic IARS1 variants presenting with infantile pulmonary alveolar proteinosis, growth retardation, microcephaly, hypotonia, developmental delay and hepatopathy; PMID 40635052 reports 14 individuals from 14 unrelated families with biallelic IARS1 variants causing a recessive multisystem syndrome that includes pulmonary alveolar proteinosis in three families.
Sources: Literature