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Common deletion and duplication syndromes v0.155 ISCA-46304-Gain Zornitza Stark Marked Region: ISCA-46304-Gain as ready
Common deletion and duplication syndromes v0.155 ISCA-46304-Gain Zornitza Stark Region: isca-46304-gain has been classified as Green List (High Evidence).
Common deletion and duplication syndromes v0.155 ISCA-46304-Gain Zornitza Stark Publications for Region: ISCA-46304-Gain were set to PMID: 29141583, 22679399
Common deletion and duplication syndromes v0.154 ISCA-46304-Gain Zornitza Stark Classified Region: ISCA-46304-Gain as Green List (high evidence)
Common deletion and duplication syndromes v0.154 ISCA-46304-Gain Zornitza Stark Region: isca-46304-gain has been classified as Green List (High Evidence).
Common deletion and duplication syndromes v0.151 ISCA-46304-Gain Sarah Milton Region: ISCA-46304-Gain was added
Region: ISCA-46304-Gain was added to Common deletion and duplication syndromes. Sources: ClinGen
Mode of inheritance for Region: ISCA-46304-Gain was set to X-LINKED: hemizygous mutation in males, biallelic mutations in females
Publications for Region: ISCA-46304-Gain were set to PMID: 29141583, 22679399
Phenotypes for Region: ISCA-46304-Gain were set to Syndromic X-linked intellectual disability Lubs type, MONDO:0010283
Review for Region: ISCA-46304-Gain was set to GREEN
Added comment: Known Clingen triplosensitive region containing MECP2 and IRAK1. Associated with intellectual disability, seizures, hypotonia, mild dysmorphism. Typically affects males but females may be mildly affected.
Sources: ClinGen