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Craniosynostosis v1.82 KMT5B Zornitza Stark Marked gene: KMT5B as ready
Craniosynostosis v1.82 KMT5B Zornitza Stark Gene: kmt5b has been classified as Green List (High Evidence).
Craniosynostosis v1.82 KMT5B Zornitza Stark Classified gene: KMT5B as Green List (high evidence)
Craniosynostosis v1.82 KMT5B Zornitza Stark Gene: kmt5b has been classified as Green List (High Evidence).
Craniosynostosis v1.81 KMT5B Zornitza Stark edited their review of gene: KMT5B: Changed rating: GREEN
Craniosynostosis v1.81 KMT5B Zornitza Stark gene: KMT5B was added
gene: KMT5B was added to Craniosynostosis. Sources: Literature
Mode of inheritance for gene: KMT5B was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: KMT5B were set to 37086723
Phenotypes for gene: KMT5B were set to Intellectual developmental disorder, autosomal dominant 51 MIM# 617788
Added comment: PMID 37086723 reports 3 individuals from 3 unrelated families with heterozygous de novo loss‑of‑function (2 frameshift) or missense KMT5B variants presenting with syndromic craniosynostosis (metopic) with congenital onset. Variants are absent from population databases; de novo segregation confirmed.
Sources: Literature