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Osteopetrosis v0.90 LRP4 Zornitza Stark Marked gene: LRP4 as ready
Osteopetrosis v0.90 LRP4 Zornitza Stark Gene: lrp4 has been classified as Green List (High Evidence).
Osteopetrosis v0.90 LRP4 Zornitza Stark Classified gene: LRP4 as Green List (high evidence)
Osteopetrosis v0.90 LRP4 Zornitza Stark Gene: lrp4 has been classified as Green List (High Evidence).
Osteopetrosis v0.89 LRP4 Zornitza Stark gene: LRP4 was added
gene: LRP4 was added to Osteopetrosis. Sources: Literature
Mode of inheritance for gene: LRP4 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: LRP4 were set to 32286743; 35052419; 40824295
Phenotypes for gene: LRP4 were set to Sclerosteosis 2, MIM# 614305
Review for gene: LRP4 was set to GREEN
Added comment: PMIDs 32286743, 35052419 and 40824295 report 3 individuals from 3 unrelated families with autosomal recessive loss‑of‑function LRP4 variants causing sclerosteosis (high bone mass, cranial hyperostosis, facial dysmorphism, syndactyly, hearing loss). Functional data include a mouse Lrp4 knock‑in model recapitulating the high bone‑mass phenotype.
Sources: Literature