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Genomic screening in children: BabyScreen+ v0.46 MEN1 Zornitza Stark Tag cancer tag was added to gene: MEN1.
Tag treatable tag was added to gene: MEN1.
Genomic screening in children: BabyScreen+ v0.44 MEN1 Zornitza Stark Marked gene: MEN1 as ready
Genomic screening in children: BabyScreen+ v0.44 MEN1 Zornitza Stark Gene: men1 has been classified as Green List (High Evidence).
Genomic screening in children: BabyScreen+ v0.44 MEN1 Zornitza Stark Classified gene: MEN1 as Green List (high evidence)
Genomic screening in children: BabyScreen+ v0.44 MEN1 Zornitza Stark Gene: men1 has been classified as Green List (High Evidence).
Genomic screening in children: BabyScreen+ v0.43 MEN1 Zornitza Stark gene: MEN1 was added
gene: MEN1 was added to Genomic screening in children: BabyScreen+. Sources: Expert Review
Mode of inheritance for gene: MEN1 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Phenotypes for gene: MEN1 were set to Multiple endocrine neoplasia 1, MIM#131100
Review for gene: MEN1 was set to GREEN
Added comment: Rated as 'strong actionability' in paediatric patients by ClinGen.

Parathyroid tumors, which cause PHPT, are the most common feature and the first clinical manifestation in 90% of individuals with MEN1 with onset typically between ages 20 and 25 years. Almost all (95-100%) individuals with MEN1 can expect to have PHPT by age 50 years. However, MEN1 affects all age groups, with a reported age range of 5 to 81 years; 17% of MEN1 tumors are diagnosed under age 21. Untreated patients with MEN1 have a decreased life expectancy with a 50% probability of death by age 50. The cause of death in 50-70% of cases is due to a malignant tumor process or sequelae of the disease, with malignancies accounting for 30% of all deaths.

Surveillance generally recommended 5yo onwards.
Sources: Expert Review