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Monogenic Diabetes v0.196 MFN2 Chirag Patel Marked gene: MFN2 as ready
Monogenic Diabetes v0.196 MFN2 Chirag Patel Gene: mfn2 has been classified as Green List (High Evidence).
Monogenic Diabetes v0.196 MFN2 Chirag Patel Classified gene: MFN2 as Green List (high evidence)
Monogenic Diabetes v0.196 MFN2 Chirag Patel Gene: mfn2 has been classified as Green List (High Evidence).
Monogenic Diabetes v0.195 MFN2 Chirag Patel gene: MFN2 was added
gene: MFN2 was added to Monogenic Diabetes. Sources: ClinGen
Mode of inheritance for gene: MFN2 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: MFN2 were set to 8458227, 26114802, 26085578, 37162328, 28414270, 30158064
Phenotypes for gene: MFN2 were set to Multiple symmetric lipomatosis with partial lipodystrophy, MONDO:1060153
Review for gene: MFN2 was set to GREEN
Added comment: ClinGen DEFINITIVE (Sep 2025)
https://search.clinicalgenome.org/CCID:008970

All reported affected individuals carry p.Arg707Trp on one allele (they are either homozygous or compound het) - gnomAD v4.1 FAF 0.05440%
Sources: ClinGen