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Cataract v0.572 MVK Zornitza Stark Marked gene: MVK as ready
Cataract v0.572 MVK Zornitza Stark Gene: mvk has been classified as Green List (High Evidence).
Cataract v0.572 MVK Zornitza Stark Classified gene: MVK as Green List (high evidence)
Cataract v0.572 MVK Zornitza Stark Gene: mvk has been classified as Green List (High Evidence).
Cataract v0.571 MVK Zornitza Stark gene: MVK was added
gene: MVK was added to Cataract. Sources: Literature
Mode of inheritance for gene: MVK was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: MVK were set to 33917151
Phenotypes for gene: MVK were set to Mevalonic aciduria, MIM# 610377
Review for gene: MVK was set to GREEN
Added comment: PMID 33917151 reports on a large cohort of individuals with MVK-related disease in an attempt to establish genotype-phenotype correlations. This includes 15 individuals with homozygous missense MVK variants (p.Leu264Phe, p.Ala334Thr) presenting with cataract. All seven patients homozygous for p.Leu264Phe had cataract and 13 of 15 cataract patients carried either p.Leu264Phe or p.Ala334Thr.
Sources: Literature