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Mendeliome v2.412 NOTCH3 chirag patel Marked gene: NOTCH3 as ready
Mendeliome v2.412 NOTCH3 chirag patel Gene: notch3 has been classified as Green List (High Evidence).
Mendeliome v2.412 chirag patel Copied gene NOTCH3 from panel Skeletal dysplasia
Mendeliome v2.412 NOTCH3 chirag patel gene: NOTCH3 was added
gene: NOTCH3 was added to Mendeliome. Sources: Expert Review Green,Literature
Mode of inheritance for gene: NOTCH3 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: NOTCH3 were set to 25394726,40256810; 32141180; 26754023
Phenotypes for gene: NOTCH3 were set to Lateral meningocele syndrome, MONDO:0007537
Mendeliome v0.4793 Zornitza Stark removed gene:NOTCH3 from the panel
Mendeliome v0.4106 NOTCH3 Zornitza Stark Classified gene: NOTCH3 as No list
Mendeliome v0.4106 NOTCH3 Zornitza Stark Gene: notch3 has been removed from the panel.
Mendeliome v0.4091 NOTCH3 Eleanor Williams gene: NOTCH3 was added
gene: NOTCH3 was added to Mendeliome. Sources: Literature
Mode of inheritance for gene: NOTCH3 was set to MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Publications for gene: NOTCH3 were set to 31960911
Phenotypes for gene: NOTCH3 were set to CADASIL
Review for gene: NOTCH3 was set to AMBER
Added comment: PMID: 31960911 - Gravesteijn et al 2020 - describe a family with a unique cysteine-altering NOTCH3 variant in exon 9 in 5 individuals, which is predicted to cause natural exon 9 skipping. This mimics the therapeutic NOTCH3 cysteine correction approach and allows the effect of cysteine corrective exon skipping on NOTCH3 protein aggregation and disease severity in humans to be studied. In this family the CADASIL phenotype was mild.

Note this gene is rated green on the Neurodegenerative disorders - adult onset panel in the Genomics England instance of PanelApp https://panelapp.genomicsengland.co.uk/panels/474/gene/NOTCH3/
Sources: Literature