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Hereditary Spastic Paraplegia v2.99 NRCAM Bryony Thompson Marked gene: NRCAM as ready
Hereditary Spastic Paraplegia v2.99 NRCAM Bryony Thompson Gene: nrcam has been classified as Green List (High Evidence).
Hereditary Spastic Paraplegia v2.99 NRCAM Bryony Thompson Classified gene: NRCAM as Green List (high evidence)
Hereditary Spastic Paraplegia v2.99 NRCAM Bryony Thompson Gene: nrcam has been classified as Green List (High Evidence).
Hereditary Spastic Paraplegia v2.98 NRCAM Bryony Thompson gene: NRCAM was added
gene: NRCAM was added to Hereditary Spastic Paraplegia. Sources: Literature
Mode of inheritance for gene: NRCAM was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: NRCAM were set to 36606341; 35108495
Disease associations for gene: NRCAM were set to neurodevelopmental disorder with neuromuscular and skeletal abnormalities, MONDO:0859236
Review for gene: NRCAM was set to GREEN
Added comment: PMID 35108495 reports 10 individuals from eight families with autosomal recessive loss‑of‑function variants in NRCAM causing a neurodevelopmental disorder characterised by developmental delay, hypotonia, spasticity and peripheral neuropathy; PMID 36606341 adds one further individual from a consanguineous family with a homozygous nonsense variant and motor‑predominant axonal polyneuropathy without CNS involvement.
Sources: Literature