Activity

Filter

Cancel
Date Panel Item Activity
5 actions
Speech apraxia v2.0 NSD1 Gene migrated from ENSG00000165671 to ENSG00000165671 (gene set migration)
Speech apraxia v1.40 NSD1 Hali Van Niel gene: NSD1 was added
gene: NSD1 was added to Speech apraxia. Sources: Expert List,Literature
Mode of inheritance for gene: NSD1 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: NSD1 were set to 41530369; 16001444
Phenotypes for gene: NSD1 were set to Sotos syndrome (MIM#117550)
Review for gene: NSD1 was set to RED
Added comment: Reported individual with CAS and de novo in frame deletion (Van Niel et al., 2026; PMID: 41530369), Validated diagnostic finding from VCGS clinical NATA pipeline.

While speech delay or impairment is prevalent in Sotos syndrome, Ball et al. (2005; PMID: 16001444) found errors appear to be language-related rather than motoric and therefore this is not enough to promote evidence.
Sources: Expert List, Literature
Speech apraxia v1.15 Zornitza Stark removed gene:NSD1 from the panel
Speech apraxia v1.6 NSD1 Thomas Scerri Deleted their review
Speech apraxia v1.6 NSD1 Thomas Scerri gene: NSD1 was added
gene: NSD1 was added to Speech apraxia. Sources: Expert list,Expert Review
Mode of inheritance for gene: NSD1 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Phenotypes for gene: NSD1 were set to Sotos syndrome, MIM# 117550
Review for gene: NSD1 was set to RED
Added comment: An in-house (as yet unpublished) CAS proband with a pathogenic variant.
Sources: Expert list, Expert Review