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Skeletal dysplasia v1.111 PEX6 chirag patel Marked gene: PEX6 as ready
Skeletal dysplasia v1.111 PEX6 chirag patel Gene: pex6 has been classified as Green List (High Evidence).
Skeletal dysplasia v1.111 PEX6 chirag patel changed review comment from: Variants in this gene account for 14.5% of Zellweger Spectrum Disorder patients according to GeneReviews (https://www.ncbi.nlm.nih.gov/books/NBK1448/) Genetic spectrum of 77 patients reviewed in PMID: 19877282.; to: Variants in this gene account for 14.5% of Zellweger Spectrum Disorder patients according to GeneReviews (https://www.ncbi.nlm.nih.gov/books/NBK1448/) Genetic spectrum of 77 patients reviewed in PMID: 19877282.

Newborns may have bony stippling (chondrodysplasia punctata) of the patella(e) and other long bones.
Skeletal dysplasia v1.111 chirag patel Copied gene PEX6 from panel Peroxisomal Disorders
Skeletal dysplasia v1.111 PEX6 chirag patel gene: PEX6 was added
gene: PEX6 was added to Skeletal dysplasia. Sources: Expert Review Green,Victorian Clinical Genetics Services
Mode of inheritance for gene: PEX6 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: PEX6 were set to 20301621, 19877282
Phenotypes for gene: PEX6 were set to Peroxisome biogenesis disorder 4A (Zellweger), MIM# 614862