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Additional findings_Adult v1.71 PIK3R1 Zornitza Stark Marked gene: PIK3R1 as ready
Additional findings_Adult v1.71 PIK3R1 Zornitza Stark Gene: pik3r1 has been classified as Green List (High Evidence).
Additional findings_Adult v1.71 PIK3R1 Zornitza Stark Classified gene: PIK3R1 as Green List (high evidence)
Additional findings_Adult v1.71 PIK3R1 Zornitza Stark Gene: pik3r1 has been classified as Green List (High Evidence).
Additional findings_Adult v1.70 PIK3R1 Zornitza Stark gene: PIK3R1 was added
gene: PIK3R1 was added to Additional findings_Adult. Sources: Expert list
Mode of inheritance for gene: PIK3R1 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Phenotypes for gene: PIK3R1 were set to SHORT syndrome, MIM# 269880
Review for gene: PIK3R1 was set to GREEN
Added comment: MODERATE actionability in adults by ClinGen.

Many features manifest in infancy/childhood but diagnosis may be delayed. Insulin resistance has a highly variable age at diagnosis ranging from 7-49 years. Though insulin resistance may be evident in mid-childhood or adolescence, diabetes mellitus typically does not develop until early adulthood.
Sources: Expert list