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Mendeliome v2.0 PLEKHG2 Gene migrated from ENSG00000090924 to ENSG00000090924 (gene set migration)
Mendeliome v1.4644 PLEKHG2 Rylee Peters Publications for gene: PLEKHG2 were set to 26573021
Mendeliome v1.4643 PLEKHG2 Rylee Peters reviewed gene: PLEKHG2: Rating: AMBER; Mode of pathogenicity: None; Publications: 40594583; Phenotypes: Leukodystrophy and acquired microcephaly with or without dystonia, MIM# 616763; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Mendeliome v0.1348 PLEKHG2 Zornitza Stark Classified gene: PLEKHG2 as Amber List (moderate evidence)
Mendeliome v0.1348 PLEKHG2 Zornitza Stark Gene: plekhg2 has been classified as Amber List (Moderate Evidence).
Mendeliome v0.1347 PLEKHG2 Zornitza Stark edited their review of gene: PLEKHG2: Added comment: Further family identified, promote to Amber.; Changed rating: AMBER; Changed publications: 26539891, 24001768, 26573021; Changed phenotypes: Leukodystrophy and acquired microcephaly with or without dystonia, MIM# 616763
Mendeliome v0.667 PLEKHG2 Zornitza Stark Marked gene: PLEKHG2 as ready
Mendeliome v0.667 PLEKHG2 Zornitza Stark Gene: plekhg2 has been classified as Red List (Low Evidence).
Mendeliome v0.667 PLEKHG2 Zornitza Stark gene: PLEKHG2 was added
gene: PLEKHG2 was added to Mendeliome_VCGS. Sources: Expert list
Mode of inheritance for gene: PLEKHG2 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: PLEKHG2 were set to 26573021
Phenotypes for gene: PLEKHG2 were set to Leukodystrophy and acquired microcephaly with or without dystonia, MIM# 616763
Review for gene: PLEKHG2 was set to RED
Added comment: Five individuals from two unrelated families reported, same homozygous missense variant.
Sources: Expert list