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Mendeliome v2.475 HAPLN1 Sarah Milton gene: HAPLN1 was added
gene: HAPLN1 was added to Mendeliome. Sources: Literature
Mode of inheritance for gene: HAPLN1 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: HAPLN1 were set to 42381221
Phenotypes for gene: HAPLN1 were set to Skeletal dysplasia, MONDO:0018230, HAPLN1-related
Review for gene: HAPLN1 was set to RED
Added comment: HAPLN1 encodes hyaluronan and proteoglycan link protein 1 and is a extracellular matrix protein (ECM), required for maintaining tissue architecture and integrity.

PMID 42381221 reports 4 individuals from 1 consanguineous family with a biallelic missense variant presenting with autosomal recessive skeletal dysplasia characterised by rhizomelic‑mesomelic limb shortening, platyspondyly, square iliac wings, short metacarpals. No supportive functional evidence in this paper.

Previous studies cited in above paper have noted skeletal phenotypes in mouse and zebrafish knockout models. Remains a candidate gene.
Sources: Literature
Mendeliome v2.0 PLN Gene migrated from ENSG00000198523 to ENSG00000198523 (gene set migration)
Mendeliome v0.13263 PLN Zornitza Stark Marked gene: PLN as ready
Mendeliome v0.13263 PLN Zornitza Stark Gene: pln has been classified as Green List (High Evidence).
Mendeliome v0.13263 PLN Zornitza Stark Phenotypes for gene: PLN were changed from to Cardiomyopathy, dilated, 1P, MIM# 609909; Cardiomyopathy, hypertrophic, 18 (MIM #613874)
Mendeliome v0.13262 PLN Zornitza Stark Publications for gene: PLN were set to
Mendeliome v0.13261 PLN Zornitza Stark Mode of inheritance for gene: PLN was changed from Unknown to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Mendeliome v0.13260 PLN Zornitza Stark reviewed gene: PLN: Rating: GREEN; Mode of pathogenicity: None; Publications: 33947203; Phenotypes: Cardiomyopathy, dilated, 1P, MIM# 609909, Cardiomyopathy, hypertrophic, 18 (MIM #613874); Mode of inheritance: MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Mendeliome v0.0 PLN Zornitza Stark gene: PLN was added
gene: PLN was added to Mendeliome_VCGS. Sources: Expert Review Green,Victorian Clinical Genetics Services
Mode of inheritance for gene: PLN was set to Unknown