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Skeletal dysplasia v1.26 POLR3A chirag patel Classified gene: POLR3A as Green List (high evidence)
Skeletal dysplasia v1.26 POLR3A chirag patel Gene: polr3a has been classified as Green List (High Evidence).
Skeletal dysplasia v1.25 POLR3A chirag patel Marked gene: POLR3A as ready
Skeletal dysplasia v1.25 POLR3A chirag patel Gene: polr3a has been classified as Red List (Low Evidence).
Skeletal dysplasia v1.25 POLR3A chirag patel gene: POLR3A was added
gene: POLR3A was added to Skeletal dysplasia. Sources: Literature
Mode of inheritance for gene: POLR3A was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: POLR3A were set to 30414627, 30450527, 30323018, 21671373, 10607952
Phenotypes for gene: POLR3A were set to Wiedemann-Rautenstrauch syndrome, MONDO:0009910
Review for gene: POLR3A was set to GREEN
Added comment: Multiple families reported with biallelic variants in POLR3A and Wiedemann-Rautenstrauch syndrome (WDRTS). This is a rare autosomal recessive neonatal progeroid disorder characterized by intrauterine growth retardation, failure to thrive, short stature, a progeroid appearance, generalized lipoatrophy, various skeletal anomalies, hypotonia, and variable mental impairment.
Sources: Literature