Activity

Filter

Cancel
Date Panel Item Activity
9 actions
Speech apraxia v1.38 PPP2R5D Zornitza Stark Marked gene: PPP2R5D as ready
Speech apraxia v1.38 PPP2R5D Zornitza Stark Gene: ppp2r5d has been classified as Green List (High Evidence).
Speech apraxia v1.38 PPP2R5D Zornitza Stark Classified gene: PPP2R5D as Green List (high evidence)
Speech apraxia v1.38 PPP2R5D Zornitza Stark Gene: ppp2r5d has been classified as Green List (High Evidence).
Speech apraxia v1.31 PPP2R5D Hali Van Niel changed review comment from: Individual with CAS reported with de novo nonsense variant, c.751 G > T; p.(Asp251Tyr) (Van Niel et al., 2026; PMID: 41530369). Validated diagnostic finding from VCGS clinical NATA pipeline

Mitchel et al. (2025; PMID: 39931922) report one individual with PPP2R5D variant with CAS (Supp Table 6).

Almost all individuals with a PPP2R5D variant have speech impairment, hallmark of disorder (PMID: 32074998)
Sources: Expert List, Literature; to: Individual with CAS reported with de novo missense variant, c.751 G > T; p.(Asp251Tyr) (Van Niel et al., 2026; PMID: 41530369). Validated diagnostic finding from VCGS clinical NATA pipeline

Mitchel et al. (2025; PMID: 39931922) report one individual with PPP2R5D variant with CAS (Supp Table 6).

Almost all individuals with a PPP2R5D variant have speech impairment, hallmark of disorder (PMID: 32074998)
Sources: Expert List, Literature
Speech apraxia v1.31 PPP2R5D Hali Van Niel gene: PPP2R5D was added
gene: PPP2R5D was added to Speech apraxia. Sources: Expert List,Literature
Mode of inheritance for gene: PPP2R5D was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: PPP2R5D were set to 41530369; 39931922; 32074998
Phenotypes for gene: PPP2R5D were set to Intellectual developmental disorder 35 (MIM#616355)
Review for gene: PPP2R5D was set to GREEN
Added comment: Individual with CAS reported with de novo nonsense variant, c.751 G > T; p.(Asp251Tyr) (Van Niel et al., 2026; PMID: 41530369). Validated diagnostic finding from VCGS clinical NATA pipeline

Mitchel et al. (2025; PMID: 39931922) report one individual with PPP2R5D variant with CAS (Supp Table 6).

Almost all individuals with a PPP2R5D variant have speech impairment, hallmark of disorder (PMID: 32074998)
Sources: Expert List, Literature
Speech apraxia v1.16 Zornitza Stark removed gene:PPP2R5D from the panel
Speech apraxia v1.6 PPP2R5D Thomas Scerri Deleted their review
Speech apraxia v1.6 PPP2R5D Thomas Scerri gene: PPP2R5D was added
gene: PPP2R5D was added to Speech apraxia. Sources: Expert list,Expert Review
Mode of inheritance for gene: PPP2R5D was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Phenotypes for gene: PPP2R5D were set to Houge-Janssens syndrome 1, MIM# 616355
Review for gene: PPP2R5D was set to RED
Added comment: An in-house (as yet unpublished) CAS proband with a pathogenic variant.
Sources: Expert list, Expert Review