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Hereditary Neuropathy v2.8 RNASEH1 Sangavi Sivagnanasundram gene: RNASEH1 was added
gene: RNASEH1 was added to Hereditary Neuropathy. Sources: Literature
Mode of inheritance for gene: RNASEH1 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: RNASEH1 were set to 28508084; 26094573
Phenotypes for gene: RNASEH1 were set to progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal recessive 2, MONDO:0014656
Review for gene: RNASEH1 was set to GREEN
Added comment: At least 4 unrelated individuals reported with biallelic variants in RNASEH1 presenting with PEO and neuropathy (sensory/motor neuropathy). Three of the reported individuals with neuropathy were confirmed via EMG.
Sources: Literature