Activity

Filter

Cancel
Date Panel Item Activity
1 actions
Genomic newborn screening: ICoNS v0.35 RPS24 Jorune Balciuniene gene: RPS24 was added
gene: RPS24 was added to Genomic newborn screening: ICoNS. Sources: Literature
Mode of inheritance for gene: RPS24 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: RPS24 were set to 39568018, 17186470, 25946618
Phenotypes for gene: RPS24 were set to Diamond-blackfan anemia 3
Penetrance for gene: RPS24 were set to unknown
Review for gene: RPS24 was set to GREEN
Added comment: Accounts for 2-3% of all DBA.

More than 90% of DBA patients present during the first year of life. The diagnosis is generally made at 3 months, of age with a range from birth to adulthood.

Treatment: Corticosteroids and red blood cell transfusions are the mainstays of therapy. Curative treatment - hematopoietic stem cell transplantation
Sources: Literature