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Genomic newborn screening: ICoNS v0.38 RPS26 Lilian Downie Marked gene: RPS26 as ready
Genomic newborn screening: ICoNS v0.38 RPS26 Lilian Downie Gene: rps26 has been classified as Green List (High Evidence).
Genomic newborn screening: ICoNS v0.38 RPS26 Lilian Downie Classified gene: RPS26 as Green List (high evidence)
Genomic newborn screening: ICoNS v0.38 RPS26 Lilian Downie Gene: rps26 has been classified as Green List (High Evidence).
Genomic newborn screening: ICoNS v0.35 RPS26 Jorune Balciuniene gene: RPS26 was added
gene: RPS26 was added to Genomic newborn screening: ICoNS. Sources: Literature
Mode of inheritance for gene: RPS26 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: RPS26 were set to 20301769, 30503522
Phenotypes for gene: RPS26 were set to Diamond-Blackfan anemia 10
Penetrance for gene: RPS26 were set to unknown
Review for gene: RPS26 was set to GREEN
Added comment: Accounts for 6-9% of all DBA.
Penetrance high, variable expressivity

More than 90% of DBA patients present during the first year of life. The diagnosis is generally made at 3 months, of age with a range from birth to adulthood.

Treatment: Corticosteroids and red blood cell transfusions are the mainstays of therapy. Curative treatment - hematopoietic stem cell transplantation
Sources: Literature