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Cardiomyopathy_Paediatric v1.19 SUCLG1 Zornitza Stark Marked gene: SUCLG1 as ready
Cardiomyopathy_Paediatric v1.19 SUCLG1 Zornitza Stark Gene: suclg1 has been classified as Green List (High Evidence).
Cardiomyopathy_Paediatric v1.19 SUCLG1 Zornitza Stark Classified gene: SUCLG1 as Green List (high evidence)
Cardiomyopathy_Paediatric v1.19 SUCLG1 Zornitza Stark Gene: suclg1 has been classified as Green List (High Evidence).
Cardiomyopathy_Paediatric v1.18 SUCLG1 Zornitza Stark gene: SUCLG1 was added
gene: SUCLG1 was added to Cardiomyopathy_Paediatric. Sources: Literature
Mode of inheritance for gene: SUCLG1 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: SUCLG1 were set to 26475597
Phenotypes for gene: SUCLG1 were set to mitochondrial DNA depletion syndrome 9, MONDO:0009504
Review for gene: SUCLG1 was set to GREEN
Added comment: PMID 26475597 reports 21 individuals from 5 families with biallelic SUCLG1 variants presenting with mitochondrial DNA depletion syndrome 9, characterised by infantile encephalomyopathy, lactic acidosis, hypotonia and hypertrophic cardiomyopathy. Cardiomyopathy was present in around 15%.
Sources: Literature