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Mitochondrial disease v0.1296 SUCLG2 Zornitza Stark Marked gene: SUCLG2 as ready
Mitochondrial disease v0.1296 SUCLG2 Zornitza Stark Gene: suclg2 has been classified as Red List (Low Evidence).
Mitochondrial disease v0.1296 SUCLG2 Zornitza Stark gene: SUCLG2 was added
gene: SUCLG2 was added to Mitochondrial disease. Sources: Literature
Mode of inheritance for gene: SUCLG2 was set to MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Publications for gene: SUCLG2 were set to 33484326
Phenotypes for gene: SUCLG2 were set to Mitochondrial disease, MONDO:0044970
Review for gene: SUCLG2 was set to RED
Added comment: PMID 33484326 reports 3 individuals from 3 unrelated families with a heterozygous nonsense c.235G>T (p.Glu79*) variant in SUCLG2 presenting with MELAS syndrome (mitochondrial encephalopathy, lactic acidosis, stroke-like episodes). No functional or segregation data are provided. Note 3 hets in gnomAD v4, hence RED rating.
Sources: Literature