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Cataract v0.622 TENM3 Zornitza Stark Marked gene: TENM3 as ready
Cataract v0.622 TENM3 Zornitza Stark Gene: tenm3 has been classified as Amber List (Moderate Evidence).
Cataract v0.622 TENM3 Zornitza Stark Classified gene: TENM3 as Amber List (moderate evidence)
Cataract v0.622 TENM3 Zornitza Stark Gene: tenm3 has been classified as Amber List (Moderate Evidence).
Cataract v0.621 TENM3 Zornitza Stark gene: TENM3 was added
gene: TENM3 was added to Cataract. Sources: Literature
Mode of inheritance for gene: TENM3 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: TENM3 were set to 36911040; 32799327
Phenotypes for gene: TENM3 were set to Microphthalmia, syndromic 15, MIM# 615145
Review for gene: TENM3 was set to AMBER
Added comment: PMID 32799327 reports a family with a homozygous nonsense TENM3 variant causing congenital cataract, microphthalmia and coloboma. PMID 36911040 reports 2 unrelated families with biallelic TENM3 variants; family 1 has congenital cataract, microphthalmia, microcephaly and developmental delay, family 2 has esotropia with speech and motor delay.
Sources: Literature