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Deafness_IsolatedAndComplex v1.335 TNC Zornitza Stark Publications for gene: TNC were set to 23936043
Deafness_IsolatedAndComplex v1.334 TNC Zornitza Stark Classified gene: TNC as Green List (high evidence)
Deafness_IsolatedAndComplex v1.334 TNC Zornitza Stark Gene: tnc has been classified as Green List (High Evidence).
Deafness_IsolatedAndComplex v1.333 TNC Zornitza Stark edited their review of gene: TNC: Added comment: Five additional unrelated families (12 patients) with heterozygous loss‑of‑function TNC variants (frameshift c.5738_5745dup, nonsense c.1615C>T, nonsense c.1641C>A, missense c.2852C>T, splice‑site c.5247A>T) reported in association with deafness. Phenotypes range from childhood‑onset fluctuating loss to adult low‑frequency progressive loss. Two of the variants are present at relatively high pop frequencies in gnomAD.; Changed rating: GREEN; Changed publications: 23936043, 40203778, 39720982, 39020321, 38640279, 35062939
Deafness_IsolatedAndComplex v0.218 TNC Zornitza Stark Marked gene: TNC as ready
Deafness_IsolatedAndComplex v0.218 TNC Zornitza Stark Gene: tnc has been classified as Amber List (Moderate Evidence).
Deafness_IsolatedAndComplex v0.218 TNC Zornitza Stark Phenotypes for gene: TNC were changed from to Deafness, autosomal dominant 56, MIM# 615629
Deafness_IsolatedAndComplex v0.217 TNC Zornitza Stark Publications for gene: TNC were set to
Deafness_IsolatedAndComplex v0.216 TNC Zornitza Stark Mode of inheritance for gene: TNC was changed from Unknown to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Deafness_IsolatedAndComplex v0.215 TNC Zornitza Stark Classified gene: TNC as Amber List (moderate evidence)
Deafness_IsolatedAndComplex v0.215 TNC Zornitza Stark Gene: tnc has been classified as Amber List (Moderate Evidence).
Deafness_IsolatedAndComplex v0.214 TNC Zornitza Stark reviewed gene: TNC: Rating: AMBER; Mode of pathogenicity: None; Publications: 23936043; Phenotypes: Deafness, autosomal dominant 56, MIM# 615629; Mode of inheritance: MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Deafness_IsolatedAndComplex v0.0 TNC Zornitza Stark gene: TNC was added
gene: TNC was added to Deafness_MelbourneGenomics_VCGS. Sources: Expert Review Green,Victorian Clinical Genetics Services,Melbourne Genomics Health Alliance Deafness Flagship
Mode of inheritance for gene: TNC was set to Unknown