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Cataract v0.593 TONSL Zornitza Stark Marked gene: TONSL as ready
Cataract v0.593 TONSL Zornitza Stark Gene: tonsl has been classified as Green List (High Evidence).
Cataract v0.593 TONSL Zornitza Stark Classified gene: TONSL as Green List (high evidence)
Cataract v0.593 TONSL Zornitza Stark Gene: tonsl has been classified as Green List (High Evidence).
Cataract v0.592 TONSL Zornitza Stark gene: TONSL was added
gene: TONSL was added to Cataract. Sources: Literature
Mode of inheritance for gene: TONSL was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: TONSL were set to 30773277
Phenotypes for gene: TONSL were set to Spondyloepimetaphyseal dysplasia, sponastrime type, MIM# 271510
Review for gene: TONSL was set to GREEN
Added comment: PMID 30773277 reports 9 individuals from 8 unrelated families with bi‑allelic TONSL variants causing Sponastrime dysplasia, a skeletal dysplasia characterised by disproportionate short stature, platyspondyly, metaphyseal striations and, in three families, childhood bilateral cataracts.
Sources: Literature