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Arthrogryposis v0.571 TSEN54 Zornitza Stark Marked gene: TSEN54 as ready
Arthrogryposis v0.571 TSEN54 Zornitza Stark Gene: tsen54 has been classified as Green List (High Evidence).
Arthrogryposis v0.571 TSEN54 Zornitza Stark Phenotypes for gene: TSEN54 were changed from to Pontocerebellar hypoplasia type 2A, MIM# 277470; Pontocerebellar hypoplasia type 4, MIM# 225753
Arthrogryposis v0.570 TSEN54 Zornitza Stark Publications for gene: TSEN54 were set to
Arthrogryposis v0.569 TSEN54 Zornitza Stark Mode of inheritance for gene: TSEN54 was changed from Unknown to BIALLELIC, autosomal or pseudoautosomal
Arthrogryposis v0.568 TSEN54 Zornitza Stark changed review comment from: Well established gene-disease association.

Individuals homozygous for the common TSEN54 missense mutation A307S are reported to have a phenotype consistent with PCH2, whereas those who were compound heterozygous for A307S and a different TSEN54 mutation have a more severe phenotype consistent with PCH4.; to: Well established gene-disease association.

Individuals homozygous for the common TSEN54 missense mutation A307S are reported to have a phenotype consistent with PCH2, whereas those who were compound heterozygous for A307S and a different TSEN54 mutation have a more severe phenotype consistent with PCH4.

Multiple contractures are part of the phenotype.
Arthrogryposis v0.568 TSEN54 Zornitza Stark edited their review of gene: TSEN54: Changed publications: 18711368, 20956791, 20952379, 20301773
Arthrogryposis v0.568 Zornitza Stark Added reviews for gene TSEN54 from panel Cerebellar and Pontocerebellar Hypoplasia
Arthrogryposis v0.0 TSEN54 Zornitza Stark gene: TSEN54 was added
gene: TSEN54 was added to Arthrogryposis_VCGS. Sources: Expert Review Green,Victorian Clinical Genetics Services
Mode of inheritance for gene: TSEN54 was set to Unknown