ATXN7

ataxin 7
OMIM: 607640, ClinGen, DECIPHER

5 panels

Panel Reviews Mode of inheritance Details
5 panels

No list ATXN7 in Syndromic Retinopathy


Level 2: Ophthalmological disorders
Version 0.234

Component of the following Super Panels:

  • Retinal Disorders Superpanel
  • 1 review Unknown
    Sources
    • Expert Review Removed
    • Expert list
    • RetNet
    Tags
    • STR

    Green ATXN7_SCA7_CAG STR in Mendeliome


    Version 1.3795

    review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Expert list
    Phenotypes
    • Spinocerebellar ataxia 7 MIM#164500

    Green ATXN7_SCA7_CAG STR in Ataxia


    Level 2: Neurology and neurodevelopmental disorders
    Version 1.158

    Component of the following Super Panels:

  • Neuromuscular Superpanel
  • Progressive Neurological Conditions
  • review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Expert List
    Phenotypes
    • Spinocerebellar ataxia 7 MIM#164500

    Green ATXN7_SCA7_CAG STR in Syndromic Retinopathy


    Level 2: Ophthalmological disorders
    Version 0.234

    Component of the following Super Panels:

  • Retinal Disorders Superpanel
  • review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Literature
    Phenotypes
    • Spinocerebellar ataxia 7 MIM#164500

    Green ATXN7_SCA7_CAG STR in Repeat Disorders


    Version 0.269

    review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Expert list
    Phenotypes
    • Spinocerebellar ataxia 7 MIM#164500
    Tags
    • adult-onset