KNG1

kininogen 1
OMIM: 612358, ClinGen, DECIPHER

3 panels

Panel Reviews Mode of inheritance Details
3 panels

Green KNG1 in Bleeding and Platelet Disorders


Level 2: Haematological disorders
Version 1.78

1 review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
  • Victorian Clinical Genetics Services
Phenotypes
  • congenital high-molecular-weight kininogen deficiency, MONDO:0009234

Green KNG1 in Mendeliome


Version 1.4865

1 review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
Phenotypes
  • angioedema, hereditary, 6, MONDO:0023660
  • congenital high-molecular-weight kininogen deficiency, MONDO:0009234

Green KNG1 in Hereditary angioedema


Level 2: Immunological disorders
Version 1.11

Component of the following Super Panels:

  • Immunological disorders_SuperPanel
  • 1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Expert list
    Phenotypes
    • Hereditary angioedema-6 (HAE6), MIM#619363