LHX1

LIM homeobox 1
OMIM: 601999, ClinGen, DECIPHER

3 panels

Panel Reviews Mode of inheritance Details
3 panels

Green LHX1 in Congenital anomalies of the kidney and urinary tract (CAKUT)


Level 2: Renal and urinary tract disorders
Version 1.1

Component of the following Super Panels:

  • Kidneyome_SuperPanel
  • 1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Literature
    • Literature
    Phenotypes
    • Mayer-Rokitansky-Kuster-Hauser syndrome, MONDO:0017771, LHX1-related

    Green LHX1 in Differences of Sex Development


    Level 2: Dysmorphic and congenital abnormality syndromes
    Version 2.2

    1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Literature
    • Literature
    Phenotypes
    • Mayer-Rokitansky-Kuster-Hauser syndrome, MONDO:0017771, LHX1-related

    Green LHX1 in Mendeliome


    Version 2.103

    1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Literature
    Phenotypes
    • Mayer-Rokitansky-Kuster-Hauser syndrome, MONDO:0017771, LHX1-related