MAMLD1

mastermind like domain containing 1
OMIM: 300120, ClinGen, DECIPHER

4 panels

Panel Reviews Mode of inheritance Details
4 panels

Green MAMLD1 in Differences of Sex Development


Level 2: Dysmorphic and congenital abnormality syndromes
Version 1.54

1 review X-LINKED: hemizygous mutation in males, biallelic mutations in females
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
Phenotypes
  • Hypospadias 2 (MIM#300758)

Green MAMLD1 in Mendeliome


Version 1.4851

2 reviews X-LINKED: hemizygous mutation in males, biallelic mutations in females
Sources
  • Expert Review Red
  • Literature
  • Expert Review Green
  • Victorian Clinical Genetics Services
Phenotypes
  • Hypospadias 2 (MIM#300758)

Red MAMLD1 in Congenital hypothyroidism

Level 3: Thyroid disorders
Level 2: Endocrine disorders
Version 0.120

1 review X-LINKED: hemizygous mutation in males, monoallelic mutations in females may cause disease (may be less severe, later onset than males)
Sources
  • Expert Review Red
  • Literature
Phenotypes
  • Congenital hypothyroidism MONDO:0018612

Green MAMLD1 in Fetal anomalies


Version 1.576

1 review X-LINKED: hemizygous mutation in males, biallelic mutations in females
Sources
  • Expert Review Green
  • Genomics England PanelApp
Phenotypes
  • Hypospadias 2 (MIM#300758)