NSMCE2

NSE2/MMS21 homolog, SMC5-SMC6 complex SUMO ligase
OMIM: 617246, ClinGen, DECIPHER

4 panels

Panel Reviews Mode of inheritance Details
4 panels

Amber NSMCE2 in Mendeliome


Version 1.4601

2 reviews BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Amber
  • Literature
Phenotypes
  • Seckel syndrome 10, MONDO:0014991

Amber NSMCE2 in Microcephaly


Level 2: Dysmorphic and congenital abnormality syndromes
Version 1.421

2 reviews BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Amber
  • Literature
Phenotypes
  • Seckel syndrome 10, MONDO:0014991

Amber NSMCE2 in Monogenic Diabetes


Level 2: Endocrine disorders
Version 0.204

Component of the following Super Panels:

  • Metabolic Disorders Superpanel
  • 2 reviews BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Amber
    • Literature
    • Literature
    Phenotypes
    • Seckel syndrome 10, MONDO:0014991

    Amber NSMCE2 in Growth failure


    Version 1.99

    2 reviews BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Amber
    • Literature
    • Literature
    Phenotypes
    • Seckel syndrome 10, MONDO:0014991