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Clefting disorders v1.128 CECR2 Zornitza Stark Marked gene: CECR2 as ready
Clefting disorders v1.128 CECR2 Zornitza Stark Gene: cecr2 has been classified as Amber List (Moderate Evidence).
Clefting disorders v1.128 CECR2 Zornitza Stark Classified gene: CECR2 as Amber List (moderate evidence)
Clefting disorders v1.128 CECR2 Zornitza Stark Gene: cecr2 has been classified as Amber List (Moderate Evidence).
Clefting disorders v1.127 CECR2 Zornitza Stark gene: CECR2 was added
gene: CECR2 was added to Clefting disorders. Sources: Literature
Mode of inheritance for gene: CECR2 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: CECR2 were set to 41964217
Phenotypes for gene: CECR2 were set to Neurodevelopmental disorder, MONDO:0700092, CECR2-related
Review for gene: CECR2 was set to AMBER
Added comment: PMID 41964217 reports six individuals from six unrelated families with heterozygous CECR2 variants (three truncating loss‑of‑function and three missense) presenting with a neurodevelopmental disorder characterised by developmental delay, speech delay, growth restriction, microcephaly, intellectual disability and, in two individuals, cleft lip/palate.
Sources: Literature