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Adrenal insufficiency v0.64 HSD17B4 Chirag Patel Marked gene: HSD17B4 as ready
Adrenal insufficiency v0.64 HSD17B4 Chirag Patel Gene: hsd17b4 has been classified as Green List (High Evidence).
Adrenal insufficiency v0.64 HSD17B4 Chirag Patel Classified gene: HSD17B4 as Green List (high evidence)
Adrenal insufficiency v0.64 HSD17B4 Chirag Patel Gene: hsd17b4 has been classified as Green List (High Evidence).
Adrenal insufficiency v0.63 HSD17B4 Chirag Patel gene: HSD17B4 was added
gene: HSD17B4 was added to Adrenal insufficiency. Sources: Literature,ClinGen
Mode of inheritance for gene: HSD17B4 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: HSD17B4 were set to 40416444; 32904102; 32528852
Phenotypes for gene: HSD17B4 were set to d-bifunctional protein deficiency, MONDO:0009855
Review for gene: HSD17B4 was set to GREEN
Added comment: ClinGen DEFINITIVE association with disease (Apr 2020).

Adrenal insufficiency reported in 5 individuals from 3 unrelated families with D‑bifunctional protein deficiency due to biallelic loss‑of‑function HSD17B4 variants.
Sources: Literature, ClinGen