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Adrenal insufficiency v0.60 IARS2 Chirag Patel Marked gene: IARS2 as ready
Adrenal insufficiency v0.60 IARS2 Chirag Patel Gene: iars2 has been classified as Amber List (Moderate Evidence).
Adrenal insufficiency v0.60 IARS2 Chirag Patel Classified gene: IARS2 as Amber List (moderate evidence)
Adrenal insufficiency v0.60 IARS2 Chirag Patel Gene: iars2 has been classified as Amber List (Moderate Evidence).
Adrenal insufficiency v0.59 IARS2 Chirag Patel gene: IARS2 was added
gene: IARS2 was added to Adrenal insufficiency. Sources: Literature
Mode of inheritance for gene: IARS2 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: IARS2 were set to 30419932
Phenotypes for gene: IARS2 were set to cataract-growth hormone deficiency-sensory neuropathy-sensorineural hearing loss-skeletal dysplasia syndrome, MONDO:0014455
Review for gene: IARS2 was set to AMBER
Added comment: Established gene-disease association with cataract‑growth hormone deficiency‑sensory neuropathy‑sensorineural hearing loss‑skeletal dysplasia (CAGSSS) syndrome.

PMID 30419932 reports 2 unrelated individuals with the same homozygous missense variant in IARS2 gene (p.Pro909Ser) presenting with CAGSSS syndrome and central adrenal insufficiency.
Sources: Literature