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Intellectual disability syndromic and non-syndromic v1.774 KLHL15 Zornitza Stark Publications for gene: KLHL15 were set to 25644381; 24817631
Intellectual disability syndromic and non-syndromic v1.773 KLHL15 Zornitza Stark Classified gene: KLHL15 as Green List (high evidence)
Intellectual disability syndromic and non-syndromic v1.773 KLHL15 Zornitza Stark Gene: klhl15 has been classified as Green List (High Evidence).
Intellectual disability syndromic and non-syndromic v1.772 KLHL15 Zornitza Stark edited their review of gene: KLHL15: Added comment: Additional male individual presenting with impaired intelligence, short stature, frequent hypoglycaemia and periodic fever.
Hemizygous variant was identified in the proband c.736 C>T p.(Arg246*) - absent from gnomAD v4.1; Changed rating: GREEN; Changed publications: 25644381, 24817631, 37452054; Changed phenotypes: intellectual disability, X-linked 103 MONDO:0010508
Intellectual disability syndromic and non-syndromic v0.1489 KLHL15 Zornitza Stark Marked gene: KLHL15 as ready
Intellectual disability syndromic and non-syndromic v0.1489 KLHL15 Zornitza Stark Gene: klhl15 has been classified as Amber List (Moderate Evidence).
Intellectual disability syndromic and non-syndromic v0.1489 KLHL15 Zornitza Stark Classified gene: KLHL15 as Amber List (moderate evidence)
Intellectual disability syndromic and non-syndromic v0.1489 KLHL15 Zornitza Stark Gene: klhl15 has been classified as Amber List (Moderate Evidence).
Intellectual disability syndromic and non-syndromic v0.1488 KLHL15 Zornitza Stark gene: KLHL15 was added
gene: KLHL15 was added to Intellectual disability, syndromic and non-syndromic_GHQ_VCGS. Sources: Literature
Mode of inheritance for gene: KLHL15 was set to X-LINKED: hemizygous mutation in males, biallelic mutations in females
Publications for gene: KLHL15 were set to 25644381; 24817631
Phenotypes for gene: KLHL15 were set to Mental retardation, X-linked 103, MIM#300982
Review for gene: KLHL15 was set to AMBER
Added comment: Two families described: variants maternally inherited in both, one deletion, the other truncating.
Sources: Literature