FDFT1

farnesyl-diphosphate farnesyltransferase 1
OMIM: 184420, ClinGen, DECIPHER

7 panels

Panel Reviews Mode of inheritance Details
7 panels

Green FDFT1 in Ichthyosis and Porokeratosis


Level 2: Dermatological disorders
Version 1.22

1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Literature
Phenotypes
  • porokeratosis MONDO:0006602, FDFT1-related
Tags
  • somatic

Green FDFT1 in Mendeliome


Version 1.3795

1 review BOTH monoallelic and biallelic (but BIALLELIC mutations cause a more SEVERE disease form), autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
Phenotypes
  • squalene synthase deficiency MONDO:0032566
  • porokeratosis MONDO:0006602, FDFT1-related

Green FDFT1 in Genetic Epilepsy


Level 2: Neurology and neurodevelopmental disorders
Version 1.307

Component of the following Super Panels:

  • Progressive Neurological Conditions
  • 2 reviews BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • Expert Review Green
    • Victorian Clinical Genetics Services
    • Australian Genomics Health Alliance Epilepsy Flagship
    Phenotypes
    • Squalene synthase deficiency, MIM# 618156

    Green FDFT1 in Autoinflammatory Disorders


    Level 2: Immunological disorders
    Version 2.40

    Component of the following Super Panels:

  • Immunological disorders_SuperPanel
  • 1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Literature
    • Expert Review Green
    • Expert Review Green
    • Literature
    Phenotypes
    • porokeratosis MONDO:0006602, FDFT1-related
    Tags
    • somatic

    Green FDFT1 in Intellectual disability syndromic and non-syndromic


    Level 2: Neurology and neurodevelopmental disorders
    Version 1.497

    1 review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • Expert list
    Phenotypes
    • Squalene synthase deficiency, MIM#618156

    Green FDFT1 in Miscellaneous Metabolic Disorders


    Level 2: Metabolic disorders
    Version 1.59

    Component of the following Super Panels:

  • Metabolic Disorders Superpanel
  • Progressive Neurological Conditions
  • 1 review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • Expert Review
    Phenotypes
    • squalene synthase deficiency MONDO:0032566

    Green FDFT1 in Mosaic skin disorders


    Level 2: Dermatological disorders
    Version 1.15

    Component of the following Super Panels:

  • Vascular Malformations SuperPanel
  • 1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Literature
    • Expert Review Green
    • Expert Review Green
    • Literature
    Phenotypes
    • porokeratosis MONDO:0006602, FDFT1-related
    Tags
    • somatic