NRXN1

neurexin 1
OMIM: 600565, ClinGen, DECIPHER

6 panels

Panel Reviews Mode of inheritance Details
6 panels

Green NRXN1 in Autism


Level 2: Neurology and neurodevelopmental disorders
Version 1.13

2 reviews BOTH monoallelic and biallelic (but BIALLELIC mutations cause a more SEVERE disease form), autosomal or pseudoautosomal
Sources
  • Literature
  • Expert Review Green
Phenotypes
  • Pitt-Hopkins-like syndrome 2 - MIM#614325
  • Complex neurodevelopmental disorder, MONDO:0100038, NRXN1-related

Green NRXN1 in Mendeliome


Version 2.336

3 reviews BOTH monoallelic and biallelic (but BIALLELIC mutations cause a more SEVERE disease form), autosomal or pseudoautosomal
Sources
  • Literature
  • Expert Review Green
Phenotypes
  • Pitt-Hopkins-like syndrome 2 - MIM#614325
  • Complex neurodevelopmental disorder, MONDO:0100038, NRXN1-related

Green NRXN1 in Genetic Epilepsy


Level 2: Neurology and neurodevelopmental disorders
Version 2.28

Component of the following Super Panels:

  • Progressive Neurological Conditions
  • 2 reviews BOTH monoallelic and biallelic (but BIALLELIC mutations cause a more SEVERE disease form), autosomal or pseudoautosomal
    Sources
    • Literature
    • Expert Review Green
    Phenotypes
    • Pitt-Hopkins-like syndrome 2 - MIM#614325
    • Complex neurodevelopmental disorder, MONDO:0100038, NRXN1-related

    Green NRXN1 in Intellectual disability syndromic and non-syndromic


    Level 2: Neurology and neurodevelopmental disorders
    Version 2.53

    2 reviews BOTH monoallelic and biallelic (but BIALLELIC mutations cause a more SEVERE disease form), autosomal or pseudoautosomal
    Sources
    • Literature
    • Expert Review Green
    Phenotypes
    • Pitt-Hopkins-like syndrome 2 - MIM#614325
    • Complex neurodevelopmental disorder, MONDO:0100038, NRXN1-related

    Red NRXN1 in Additional findings_Paediatric


    Level 2: Screening
    Version 1.0

    0 reviews Unknown
    Sources
    • Expert Review Red
    • BabySeq Category C gene
    Phenotypes
    • Autism

    Red NRXN1 in Genomic newborn screening: BabyScreen+


    Level 2: Screening
    Version 2.0

    0 reviews Unknown
    Sources
    • BabySeq Category C gene
    • Expert Review Red
    Phenotypes
    • Autism