PAK2

p21 (RAC1) activated kinase 2
OMIM: 605022, ClinGen, DECIPHER

6 panels

Panel Reviews Mode of inheritance Details
6 panels

Red PAK2 in Congenital Heart Defect


Level 2: Cardiovascular disorders
Version 0.540

1 review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Sources
  • Literature
Phenotypes
  • ?Knobloch syndrome 2 MIM#618458

Green PAK2 in Mendeliome


Version 1.4850

2 reviews MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Literature
Phenotypes
  • Knobloch 2 syndrome, MIM#618458

Amber PAK2 in Genetic Epilepsy


Level 2: Neurology and neurodevelopmental disorders
Version 1.414

Component of the following Super Panels:

  • Progressive Neurological Conditions
  • 3 reviews MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Amber
    • Literature
    Phenotypes
    • Knobloch 2 syndrome MIM#618458

    Green PAK2 in Intellectual disability syndromic and non-syndromic


    Level 2: Neurology and neurodevelopmental disorders
    Version 1.780

    1 review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Green
    • Literature
    Phenotypes
    • Knobloch 2 syndrome MIM#618458

    Red PAK2 in Syndromic Retinopathy


    Level 2: Ophthalmological disorders
    Version 0.259

    Component of the following Super Panels:

  • Retinal Disorders Superpanel
  • 1 review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • Literature
    Phenotypes
    • Knobloch syndrome 2 MIM#618458

    Red PAK2 in Fetal anomalies


    Version 1.576

    1 review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • Literature
    Phenotypes
    • ?Knobloch syndrome 2 MIM#618458