Description
This panel was developed and is maintained by VCGS.

7 reviewers

  • Zornitza Stark (Victorian Clinical Genetics Services)

  • chirag patel (Genetic Health Queensland)

  • Bryony Thompson (Royal Melbourne Hospital)

  • Elena Savva (Victorian Clinical Genetics Services)

  • Ivan Macciocca (Victorian Clinical Genetics Services)

  • Sangavi Sivagnanasundram (Melbourne Health)

  • Natasha Henden (Ingles Lab, Garvan Institute of Medical Research)

23 Entities

23 reviewed, 1 green

List Entity Reviews Mode of inheritance Details
23 Entitiess
Green Green List (high evidence)
SCN5A
3 reviews
3 green
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Victorian Clinical Genetics Services
Phenotypes
  • SCN5A-related cardiac rhythm disorder MONDO:1010181
  • Brugada syndrome
  • Multifocal ectopic Purkinje-related premature contractions (MEPPC) syndrome
Tags
Red Red List (low evidence)
ABCC9
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
ANK2
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
CACNA1C
1 review
1 red
Unknown
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Tags
  • disputed
Red Red List (low evidence)
CACNA2D1
1 review
1 red
Unknown
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Phenotypes
  • Brugada syndrome 1, MONDO:0011001
Tags
  • disputed
Red Red List (low evidence)
CACNB2
1 review
1 red
Unknown
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Tags
  • disputed
Red Red List (low evidence)
FGF12
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
Phenotypes
  • Brugada syndrome MONDO:0015263
Tags
Red Red List (low evidence)
GPD1L
3 reviews
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Phenotypes
  • Brugada syndrome 2, MIM# 611777
Tags
  • disputed
Red Red List (low evidence)
HCN4
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
KCND3
1 review
1 red
Unknown
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Phenotypes
  • Brugada syndrome
Tags
  • disputed
Red Red List (low evidence)
KCNE3
1 review
1 red
Unknown
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
KCNE5
1 review
1 red
X-LINKED: hemizygous mutation in males, biallelic mutations in females
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
KCNH2
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
KCNJ8
1 review
1 red
Unknown
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Phenotypes
  • Brugada syndrome 1, MONDO:0011001
Tags
  • disputed
Red Red List (low evidence)
PKP2
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
RANGRF
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • refuted
Red Red List (low evidence)
SCN10A
1 review
1 red
Unknown
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Phenotypes
  • Brugada syndrome
Tags
  • disputed
Red Red List (low evidence)
SCN1B
1 review
1 red
Unknown
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Phenotypes
  • Brugada syndrome 1, MONDO:0011001
Tags
  • disputed
Red Red List (low evidence)
SCN2B
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
SCN3B
2 reviews
2 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Red
  • Victorian Clinical Genetics Services
Phenotypes
  • Brugada syndrome 7 MIM#613120
Tags
  • disputed
Red Red List (low evidence)
SLMAP
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed
Red Red List (low evidence)
TMEM168
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
Phenotypes
  • Brugada syndrome MONDO:0015263
Tags
Red Red List (low evidence)
TRPM4
1 review
1 red
MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • ClinGen
  • Expert Review Red
Phenotypes
  • Brugada syndrome, MONDO:0015263
Tags
  • disputed

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